The syndrome of persistence of Mullerian derivatives is a rare form of internal male pseudohermaphrodism. It is characterized by the presence of the uterus, tubes and upper vagina in a boy otherwise normally virilized with a karyotype 46 XY. It is the consequence of a deficit in anti-Mullerian hormone or an abnormality of its receptors. We report a case of intraoperative discovery during a diagnostic laparoscopy for non-palpable cryptorchid testes.